Palabras clave: atrofia de múltiples sistemas (AMS), disautonomía, ataxia cerebelosa, el síndrome de Shy- Drager, la degeneración nigroestriada. (SND) y la. Shy-Drager syndrome a case report with polysomnography. Síndrome de Shy- Drager: registro de caso com estudo polissonográfico. F. S. Aloe; P.E. Marchiori; . A atrofia de múltiplos sistemas (AMS) é uma doença neurodegenerativa esporádica nigro-estriatal, atrofia olivopontocerebelar, síndrome de Shy- Drager.

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It is hard to establish the differential diagnosis with Parkinson’s disease, as it can be seen in our case.

Shy Drager syndrome.

The actual consensus tries to define the diagnostic criterions and recommends the term MSA-P when parkinsonian features predominate, and the term MSA-C when cerebellar signs rules the clinical picture. Six months later he presented with the same complains and the same alterations on sinrrome examination except for worsing on orthostatic hypotension: How to diagnose MSA early: Our patient number 2 presented insomnia.

For bladder control problems this may be controlled with medications initially but as the disease process advances with time the patient may require catheter insertion for draining the bladder.

Our case number 2 presented putaminal hypo intensity Fig 2B as well as marginal hyper intensity Fig 2A in T2 images. Deager M – Incidenza delia ipotensione ortostatica: Both of them presented orthostatic hypotension and urinary incontinence autonomic system alterations.

Shy-Drager Syndrome: Causes, Symptoms, Treatment, Prognosis, Life Expectancy

Body functions controlled by these areas of the brain and spinal cord do not function normally in sufferers. Arterial pressure AP was X80 mmHg and radial pulse frequency 60 bpm with the patient laying down; X70 and 70bpm when standing up.

Recently, neuroimaging studies, especially the MRI, have showed some alterations that, although not specific, may help the diagnostic of different forms of MSA. These functions include the autonomic or involuntary nervous system which controls blood pressure, heart rate, and bladder function and the motor system which controls balance and muscle movement.


It is worse after meals and early in the day. J Neurol Transm ; The incidence is 0.

The maximum that a patient with known diagnosis of Shy-Drager Syndrome lives is around 10 years from the time of the diagnosis, with the patient becoming more and more dependent with time as there is progression of Shy-Drager Syndrome.

Ddrager patients complain of severe constipation and later develop rectal incontinence.

Bull J Hopk Hosp Medications to elevate blood pressure, such as salt-retaining steroids, are often necessary, but they can cause side effects and should be carefully monitored.

Categories, Symptoms, Diagnosis, Causes, Prognosis. When orthostatic hypotension becomes severe i. Slurred speech was the patients main complain, limiting his daily activity. In the second case, diffuse pain was the first symptom, probably resulting from extrapyramidal rigidity that soon became evident with clear asymmetry right side more intense than the left.

Shy-Drager Syndrome|Causes|Symptoms|Treatment|Prognosis|Life Expectancy

Not all specialists use the term “Shy-Drager” to mean precisely the same condition, and diagnostic certainty cannot at present be achieved during life. Brodal B – Neurological Anatomy. As of now there drsger no cure for Shy-Drager Syndrome and treatment is basically symptomatic and supportive aimed at controlling sindromd symptoms and the make the patient as comfortable as possible and allow the patient to be as independent as he or she can be. Cardio or Weight Training? Longitudinal MRI study of multiple system atrophy: The patient may also undergo tests to look for any autonomic dysfunction like testing the bowel and bladder function of the patient, blood pressure monitoring, ophthalmologic examination to check the status of the eyes, EMG and nerve conduction studies to check the status of the functioning of the muscles and nerves.

Ann Otol Laryngol Shy-Drager Syndrome which is also referred to as Multiple System Atrophy is an extremely why neurological condition in which the autonomic functions of the body get impaired.


Arch Intern Med Rev Clin Esp Both of them appears lately in MSA-A. Anti-parkinsonian medication, such as L-dopa may be helpful. The majority of misdiagnosis patients on the study above had in fact supranuclear palsy 4, The symptoms of parkinsonian type of Shy-Drager Syndrome are:. There is no specific treatment to MSA until the present, only symptomatic interventions Received 20 October dr, received in final form 16 January Any type of environmental toxin responsible for the development of Shy-Drager Syndrome is also being studied but as of now fe has been no proof of such.

Incontinence may be treated with medications or catheterisation. Four years later she complained of rigidity of arms and legs mainly on the right sindroke.

Progression and prognosis in multiple hsy atrophy An analysis of Japanese patients. During the final stages of the disease, patients have trouble chewing, swallowing, speaking and breathing.

These same authors refer to an early asymmetric beginning of parkinsonism in We describe two patients showing different presentations of the same disease. The probable outcome is poor. There was no rest or postural tremor, but the speech was slurred, very difficult to be understood.

Many patients also complain of dry mouth and dry skin, and because of abnormal sweating have problems with relation of body temperature. We mainly draw attention to the importance of a good neuroradiological assessment.

A medication called mestinon is quite effective in controlling the blood pressure both while standing and lying down.

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